Abstract 20
Category: Clinical Science

At the end of the session, participants will be able to:

  1. Describe the histopathology of lymphocytic hypophysitis.
  2. Describe the inflammation associated with other pituitary lesions (PitNET, cyst, apoplexy)
  3.  Summarize the (possible) pathogenesis and clinical significance of lymphocytic hypophysitis.

COI Disclosure:

None to disclose.

Presenter

Dr. Del Bigio is a Professor – Department of Pathology, University of Manitoba (since 1994).

MD 1982; PhD 1987; FRCPC (Neuropathology) 1993

Marc R. Del Bigio

Department of Pathology, University of Manitoba and Shared Health Manitoba, Winnipeg Canada

Target Audience:
Pathologists, Residents, Medical Students

CanMEDS:
Medical Expert (the integrating role), Health Advocate

Pituitary inflammatory lesions including lymphocytic hypophysitis: a 30-year single centre experience

Abstract

In Manitoba (population 1.4 million) all neurosurgical procedures and all autopsy neuropathology examinations are done at one center. In a retrospective review (1996-2025) I searched for cases with pituitary inflammation. Among 678 surgical pituitary biopsies we encountered: 15 idiopathic lymphocytic hypophysitis; 18 PitNET with inflammation; 34 PitNET + apoplexy with inflammation; 13 inflammation associated with Rathke cleft cyst; 3 bacterial infection.  Among 4768 pituitaries from autopsies we encountered: 16 idiopathic lymphocytic hypophysitis; 1 PitNET + apoplexy; 2 pituitary apoplexy without obvious cause; 3 inflammation associated with Rathke cleft cyst; 19 pituitary inflammation and associated disseminated infection (2 Herpes simplex; 5 suspected viral; 5 Mycobacterial; 7 other bacterial sepsis / meningitis).  In some autopsy cases lymphocytic hypophysitis was incidental, 1 had chronic demyelinating disease, 4 had prominent inflammation in the thyroid, and in 1 case it was considered to be a major contributor to death.  Four decedents had pre-mortem clinical endocrine syndrome (38 year female hypothyroidism; 49 year female hyperprolactinemia; 44 year male Addison disease and hypothyroidism; 49 year female diabetes mellitus).  Conclusive proof of autoimmune lymphocytic hypophysitis is elusive. PitNET, apoplexy, and cyst-associated inflammation are common and of uncertain significance.  In all specimens, complete history and imaging correlates are necessary.  Although rarely a contributor to death, examination of the pituitary gland is an important part of the autopsy in individuals who die unexpectedly, particularly if they have a history of endocrine disease or recent neurological symptoms.